Parsing ketotic hypoglycaemia

Effect of ephedrine in ketotic hypoglycaemia.

Effect of ephedrine in ketotic hypoglycaemia. The effect of oral ephedrine administration on a child with ketotic hypoglycaemia who had not responded to dietary measures alone was studied. After ephedrine administration, the hypoglycaemia developing after ketogenic stress was less profound and was substantially delayed. The impaired glycaemic response to glucagon during hypoglycaemia, character...

Diagnosis of ketotic hypoglycaemia of childhood.

Habbick, B. F., McNeish, A. S., and Stephenson, J. B. P. (1971). Archives of Disease in Childhood, 46, 295. Diagnosis of ketotic hypoglycaemia of childhood. Twenty cases of ketotic hypoglycaemia have been diagnosed in one medical unit in the past 8 years. Typically the children were 'dysmature' at birth, with a history suggesting hypoglycaemia in the first 36 hours of life, and they have remain...

Ketotic (idiopathic glucagon unresponsive) hypoglycaemia: diazoxide effects.

Long-term outcome of isobutyryl-CoA dehydrogenase deficiency diagnosed following an episode of ketotic hypoglycaemia

Isobutyryl-CoA Dehydrogenase Deficiency (IBDD) is an inherited disorder of valine metabolism caused by mutations in ACAD8. Most reported patients have been diagnosed through newborn screening programmes due to elevated C4-carnitine levels and appear clinically asymptomatic. One reported non-screened patient had dilated cardiomyopathy and anaemia at the age of two years. We report a 13 month old...

Hyperosmolar non-ketotic diabetes.

Hyperosmolar non-ketotic crises occur chiefly in mild, maturity-onset diabetics, yet present a medical emergency carrying a high mortality. This may in part be due to a lack of awareness of the clinical presentation, and of the principles of treatment. Five cases are described, in all of which excessive consumption of Lucozade, a proprietary 'glucose' drink, played an important part in the deve...